AP Target Symposium 3 (II-APT3)
Dealing with congenitally corrected transposition of the great arteries - Efforts to minimize late development of systemic ventricular dysfunction

[II-APT3-01] Morphological aspects

^○Hideki Uemura (Congenital Heart Disease Center, Nara Medical University, Japan)

It is essential to clarify the concept behind the terms ‘congenitally corrected transposition of the great arteries’, ‘discordant atrioventricular connections’, ‘l-transposition’, and so on. Overall understanding then will require recognition of morphological diversity and architectural spectra within this entity; not only for atrioventricular/ventriculo-arterial connections, but also atrial arrangement, nature of a ventricular septal defect (if any), obstruction across the ventricular outflow tracts (particularly to the pulmonary arteries), and anatomy of the coronary circulation. The feature of the conduction system has been well documented in this setting.
Such background knowledge should contribute to better comprehension of functional results of the systemic right ventricle or those subsequent to the so-called anatomic biventricular repair in the longer term. The investigators may not necessarily discuss the outcome through a uniform language. Thus, confusion or misleading analysis could go further in this difficult clinical area.