The 54th Annual Meeting of Japanese Society of Pediatric Cardiology and Cardiac Surgery

Presentation information

AEPC-JSPCCS Joint Symposium

AEPC-JSPCCS Joint Symposium(II-AEPCJS)
Congenitally corrected TGA

Fri. Jul 6, 2018 8:40 AM - 10:10 AM 第2会場 (301)

座長:坂本 喜三郎(静岡県立こども病院心臓血管外科)
座長:Gurleen Sharland(Evelina Children's Hospital)

[II-AEPCJS-01] How to assess the Tricuspid valve and RV function in CCTGA by CMR

Inga Voges (University Hospital Schleswig-Holstein, Campus Kiel, Department of Congenital Heart Disease and Paediatric Cardiology, Kiel, Germany)

Congenitally corrected Transposition of the great arteries (ccTGA) is a rare cardiac malformation characterized by the combination of discordant atrioventricular and ventriculo-arterial connections and is usually accompanied by other malformations such as ventricular septal defects, obstruction of the morphologically LV outflow tract and lesions of the tricuspid valve.
In patients with ccTGA the systemic right ventricle (RV) and its tricuspid valve are exposed to systemic arterial afterload and great concern exists about the ability of the anatomic RV to sustain the systemic circulation over the long term. Cardiovascular magnetic resonance imaging plays an important role in the evaluation of ccTGA patients during follow-up as it offers an accurate quantification of RV volumes and function as well as evaluation of the tricuspid valve.
In this presentation the various CMR methods for the detailed assessment of the systemic RV and the tricuspid valve are presented in the light of the current literature in ccTGA.