The 60th Annual Meeting of Japanese Society of Pediatric Cardiology and Cardiac Surgery

Presentation information

JCK-AP session

Arrhythmia

JCK-AP session 1 (II-JCKAP1)
Arrhythmia

Fri. Jul 12, 2024 8:00 AM - 9:30 AM ROOM 8・JCK-AP Forum (5F 502+503)

Chair:Jun Yoshimoto(Department of Electrophysiology, Shizuoka Children's Hospital )
Chair:June Huh(Department of Pediatrics, Samsung Medical Center,Sungkyunkwan University School of Medicine)

[II-JCKAP1-6] Electrophysiological Characteristics of Tachyarrhythmias and Effects of Catheter Ablation in Patients with Fontan Circulation

Ja-Kyoung Yoon1, Jae-Sun Uhm2 (1.Department of Pediatric Cardiology, Severance Hospital, College of Medicine, Yonsei University, Seoul, 2.Department of Cardiology, Severance Hospital, College of Medicine, Yonsei University, Seoul)

Keywords:Catheter ablation, Tachyarrhythmia, Fontan

Introduction: As tachyarrhythmias in congenital heart disease patients rise, catheter ablation's role grows, though it's limited in Fontan patients. This study explores the arrhythmia burden and catheter ablation's effects in these patients.Methods: Patients with Fontan circulation who underwent catheter ablation for tachyarrhythmia were reviewed. We analyzed characteristics of congenital heart disease, tachyarrhythmia mechanisms, cardiac access approaches, and the efficacy and safety of catheter ablation.Results: Twenty patients with Fontan circulation (mean age 22.8years) underwent 30 catheter ablations for tachyarrhythmia. Seven had heterotaxia syndrome (right isomerism in six, left in one). Nine had lateral tunnel Fontan and 11 had extracardiac conduit Fontan. Fontan conduit puncture succeeded in 18 of 19 cases using inferior vena cava (18 patients) and superior vena cava (1 patient) approaches. Tools used included cut stylets in 13 patients, balloons in 10, and snares in 7. Tachyarrhythmias included focal atrial tachycardia (9 cases), intraatrial macroreentrant tachycardia (IART, 6 cases), twin atrioventricular node reciprocating reentrant tachycardia (4 cases), atrioventricular nodal reentrant tachycardia (3 cases), and unknown (2 cases). Catheter ablation had a 73.3% acute success rate (22 of 30 procedures), a 5.3% recurrence rate (1 of 19 patients), and no complications (0 of 30 procedures).Conclusions: Focal atrial tachycardia and IART are the most common tachycardia mechanisms in patients with Fontan circulation. Catheter ablation is effective and safe.