The 60th Annual Meeting of Japanese Society of Pediatric Cardiology and Cardiac Surgery

Presentation information

JCK-AP session

Surgery

JCK-AP session 6-2 (III-JCKAP6-2)
Surgery 2

Sat. Jul 13, 2024 8:30 AM - 9:20 AM ROOM 8・JCK-AP Forum (5F 502+503)

Chair:Shingo Kasahara(Department of Cardiovascular Surgery,Okayama University Graduate School of Medicine, Dentistry and Pharmaceutical Sciences)
Chair:Chang Ha Lee(Sejong General Hospital)

[III-JCKAP6-2-5] Long-Term Outcomes of Modified Cone Reconstruction for Ebstein's Anomaly in a Single Center

Tae-Gook Jun, Ilkun Park, Ji-Hyuk Yang, I-Seok Kang, June Huh, Jinyoung Song (Department of Thoracic and Cardiovascular Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul)

Keywords:Ebstein anomaly, Tricuspid regurgitation, Cone reconstruction

Background and Objective: We aimed to investigate long-term clinical and echocardiographic outcomes, including tricuspid valve durability, after modified cone reconstruction in patients with Ebstein's anomaly. Methods: This was a retrospective analysis of all patients who underwent modified cone reconstruction for Ebstein's anomaly at a single tertiary center between January 2005 and June 2023.Results: A total of 35 patients underwent modified cone reconstruction for Ebstein's anomaly; the mean age was 27.1 years (range, 0.01~63.7). There were five patients (14.3%) with Carpentier type A, ten patients (28.5%) with Carpentier type B, eighteen patients with Carpentier type C (51.4%), and two patient with Carpentier type D (5.7%). Mean cardiopulmonary bypass time and aortic cross clamp time were 122.9 minutes and 88.1 minutes, respectively. Mean hospital day was 11.6 days. There was no early or late mortality. During follow-up, one patient (2.8%) underwent reoperation for tricuspid regurgitation due to leaflet perforation. Median follow-up duration was 5.0 years (range (0.2~13.1)Conclusions: Ebstein's anomaly can be repaired by modified cone reconstruction with low mortality, morbidity, and good tricuspid valve durability.