ポスター (III-P42)
外科治療 3

[III-P42-10] PEP scoreを用いたエプスタイン奇形の予後予測

^○友保 貴博, 田中 健佑, 林 秀憲, 新井 修平, 浅見 雄司, 笹原 聡豊, 池田 健太郎, 下山 伸哉, 岡 徳彦, 小林 富男, 宮本 隆司 (群馬県立小児医療センター)

キーワード：Ebstein's anomary, PEP score, echocardiography

Objective:The surgical treatment for Ebstein's anomaly has greatly progressed by the clarification of the patient's condition and the development of new therapies. We should consider the appropriate treatment strategy for the tricuspid valve and the right ventricle form and consider their individual form in and the condition of each patient.Methods:We sought to better define prenatal echographic predictors (PEP) score[top score=11;1:cardiothoracic area ratio=1p6＜0%≦0p,2:plastering level to Apex;2p＜1/3＜1p＜2/3≦0p,3:TR;mild=3p,moderate=2p,severe=1p,4:Celermajer index;2p＜0.8≦1p＜1.0≦0p,5:LV tei index;3p＜0.4≦2p＜0.5≦1p＜0.6≦0p6:Gestational age;0p＜35w≦1p].Between December 2011 and April 2016,7 fetuses were diagnosed with Ebstein's anomaly in our hospital.Results:Three patients died:at day0,5,41 after birth.Usually,the first operation is performed for a single ventricle palliation;such as Sternes operation with a PEP score of＜4,in a low score patients.Three survivors were found to have high PEP score when compared with non-survivors.Biventricular repair of Ebstein's anomaly in the critically ill neonates are feasible and the repair,such as the Cones operation,seems durable.Conclusion:PEP score demonstrates potentially novel insights into hemodynamic derangemants and their association with outsomes in patients with Ebstein's anomaly.